Clear Cell Odontogenic Carcinoma: A Case Report

Abstract

Background: Clear cell odontogenic carcinoma (CCOC) is a rare malignant epithelial odontogenic tumor of the jaws with aggressive behavior, local recurrence and distant metastases. Case report: A 39-year-old male presented with a painful swelling and a well- defined radiolucent lesion that was comparable to an inflammatory odontogenic le-sion. Investigation: Knowledge about the clinicopathological and immunohistochemical characteristics of CCOC helps to differentiating it from other clear cell tumors. Conclusions: CCOC is an unusual malignant odontogenic tumor with unknown etiology. A careful approach is suggested both clinically and immunohistochemically for definitive diagnosis. Long term follow up is necessary because of its potential for recurrence and distant metastasis.